Dermatofibrosarcoma protuberans.

نویسندگان

  • Stanley J Miller
  • Murad Alam
  • James Andersen
  • Daniel Berg
  • Christopher K Bichakjian
  • Glen Bowen
  • Richard T Cheney
  • Frank Glass
  • Roy C Grekin
  • James M Grichnik
  • Anne Kessinger
  • Nancy Y Lee
  • Stuart Lessin
  • Daniel D Lydiatt
  • Lawrence W Margolis
  • Jeffrey Michalski
  • Kishwer S Nehal
  • Paul Nghiem
  • Allan R Oseroff
  • E William Rosenberg
  • Ashok R Shaha
  • Ronald J Siegle
  • Marshall M Urist
چکیده

Overview The NCCN Non-Melanoma Skin Cancer Panel has developed these guidelines outlining the treatment of dermatofibrosarcoma protuberans (DFSP) to supplement their other guidelines (NCCN Clinical Practice Guidelines in Oncology [NCCN Guidelines] for Basal Cell and Squamous Cell Skin Cancers and Merkel Cell Carcinoma; to view the most recent version of these guidelines, visit the NCCN Web site at www.NCCN.org). The NCCN Soft Tissue Sarcoma Panel provided expert input in the development of these guidelines. DFSP is an uncommon, low-grade sarcoma of fibroblast origin with an incidence rate of 4.2 to 4.5 cases per million persons per year in the United States.1,2 It rarely metastasizes. However, initial misdiagnosis, prolonged time to accurate diagnosis, and large NCCN

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Case report: Pedunculated Dermatofibrosarcoma Protuberans from Kerman

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Imaging findings of head and neck dermatofibrosarcoma protuberans.

BACKGROUND AND PURPOSE Dermatofibrosarcoma protuberans is a rare, locally aggressive sarcoma of the skin in children and adults, usually involving the trunk and extremities and less commonly the head and neck. Despite clinical reports in the literature on the management of dermatofibrosarcoma protuberans, there are limited articles describing its imaging features. MATERIALS AND METHODS We ret...

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عنوان ژورنال:
  • Journal of the National Comprehensive Cancer Network : JNCCN

دوره 5 5  شماره 

صفحات  -

تاریخ انتشار 2007